National Prion Disease Pathology Surveillance Center Cases Examined1
(October 7, 2014)
1 Listed based on the year of death or, if not available, on year of
referral;
2 Cases with suspected prion disease for which brain tissue and/or blood
(in familial cases) were submitted;
3 Disease acquired in the United Kingdom;
4 Disease acquired in the United Kingdom in one case and in Saudi Arabia in
the other;
5 Disease possibly acquired in a Middle Eastern or Eastern European
country;
6 Includes 11 cases in which the diagnosis is pending, and 19 inconclusive
cases;
7 Includes 12 (11 from 2014) cases with type determination pending in which
the diagnosis of vCJD has been excluded.
The sporadic cases include 2660 cases of sporadic Creutzfeldt-Jakob disease
(sCJD),
50 cases of Variably Protease-Sensitive Prionopathy (VPSPr)
and 21 cases of sporadic Fatal Insomnia (sFI).
Year Total Referrals2 Prion Disease Sporadic Familial Iatrogenic vCJD
1996 & earlier 53 35 31 4 0 0
1997 114 68 59 9 0 0
1998 88 52 44 7 1 0
1999 123 74 65 8 1 0
2000 145 103 89 14 0 0
2001 212 120 110 10 0 0
2002 248 149 126 21 2 0
2003 265 167 137 30 0 0
2004 326 187 164 22 0 13
2005 343 194 157 36 1 0
2006 381 194 164 28 0 24
2007 377 213 184 29 0 0
2008 397 233 208 25 0 0
2009 421 255 213 41 1 0
2010 414 258 217 41 0 0
2011 410 256 215 41 0 0
2012 421 253 218 35 0 0
2013 439 280 221 57 1 0
2014 275 166 109 45 0 15
TOTAL 54526 32577 2731 503 7 4
http://www.cjdsurveillance.com/pdf/web_table.pdf
if you notice, if you add up the vpspr 50 cases and the sporadic FFI 21 cases, and then add to the total sporadic cjd cases of 2660, this is where the total of 2731 sporadic cases come from...seems they are lumping them all together as total sporadic cjd cases, and leaving the sporadic cjd text completly out of the picture now. smoooth. covering all bases I presume, and they moved the goal post in the middle of the game, again. niice...we all didn't fall off a shrimp boat yesterday$$$
if you notice, if you add up the vpspr 50 cases and the sporadic FFI 21 cases, and then add to the total sporadic cjd cases of 2660, this is where the total of 2731 sporadic cases come from...seems they are lumping them all together as total sporadic cjd cases, and leaving the sporadic cjd text completly out of the picture now. smoooth. covering all bases I presume, and they moved the goal post in the middle of the game, again. niice...we all didn't fall off a shrimp boat yesterday$$$
Last updated September 17,
2013
TEXAS CJD TSE PRION DISEASE SEE MAP ;
USA 4TH CASE VCJD (aka nvCJD) HUMAN MAD COW, THE SILENCE IS DEAFENING BSE,
CWD, AND SCRAPIE TSE PRION DISEASE
Greetings DSHS, Dr. Fishcer, et al,
I know that most in the USA could care less about the CJD TSE prion disease
aka mad cow type disease. but there are some of us here that will never forget.
you can cover up what ever you want. we all know. I have seen it happen too
many times here in Texas with BSE TSE prion, either the typical or the atypical
strains, or with the feed, or, with cwd, or scrapie as that goes, but we are
still here, and we will never forget...
kind regards, terry
Creutzfeld-Jacob Disease (CJD) Emerging & Acute Infectious Disease
Branch Michael Fischer
Marilyn Felkner
512-776-7676
512-776-7676
Chronic Wasting Disease Zoonosis Control Branch Eric Fonken
512-776-2155
Lab tests have confirmed a diagnosis of variant Creutzfeldt-Jakob Disease
(CJD) in a patient who recently died in Texas. Variant CJD is a rare, fatal
brain disorder, first described in 1996 in the United Kingdom and associated
with beef consumption overseas.
This is the fourth case ever reported in the United States. In each of the
three previous cases, infection likely occurred outside the United States,
including the United Kingdom and Saudi Arabia. The history of this fourth
patient includes extensive travel to Europe and the Middle East, and infection
likely occurred outside the United States. The CDC and DSHS continue to
investigate the case.
There are no Texas public health concerns or threats associated with this
case.
CDC Confirmation Information: http://www.cdc.gov/ncidod/dvrd/vcjd/other/confirmed-case-in-texas.htm
CDC Fact Sheet: http://www.cdc.gov/ncidod/dvrd/vcjd/factsheet_nvcjd.htm
Texas CJD Information: http://www.dshs.state.tx.us/idcu/disease/creutzfeldt-jakob/
Last updated June 02, 2014
CONFIRMED HUMAN BSE AKA MAD COW DISEASE vCJD TEXAS USA
CONFIRMED HUMAN BSE AKA MAD COW DISEASE vCJD TEXAS USA
Monday, June 02, 2014 Confirmed Variant CJD Case in Texas
SO, 4 months after the fact and still no word on this case. no information
what so ever. the silence is deafening $$$
Monday, November 3, 2014
The prion protein protease sensitivity, stability and seeding activity in
variably protease sensitive prionopathy brain tissue suggests molecular overlaps
with sporadic Creutzfeldt-Jakob disease
Saturday, August 14, 2010
BSE Case Associated with Prion Protein Gene
Mutation (g-h-BSEalabama) and VPSPr PRIONPATHY
Monday, June 23, 2014
PRION 2014 TYPICAL AND ATYPICAL BSE AND CJD REPORT UPDATES
Transmissible Spongiform Encephalopathy TSE Prion Disease North America
2014
Transmissible Spongiform Encephalopathy TSE Prion Disease have now been
discovered in a wide verity of species across North America. typical C-BSE,
atypical L-type BASE BSE, atypical H-type BSE, atypical H-G BSE, of the bovine,
typical and atypical Scrapie strains, in sheep and goats, with atypical Nor-98
Scrapie spreading coast to coast in about 5 years. Chronic Wasting Disease CWD
in cervid is slowly spreading without any stopping it in Canada and the USA and
now has mutated into many different strains. Transmissible Mink Encephalopathy
TME outbreaks. These Transmissible Spongiform Encephalopathy TSE Prion Disease
have been silently mutating and spreading in different species in North America
for decades.
The USDA, FDA, et al have assured us of a robust Triple BSE TSE prion
Firewall, of which we now know without a doubt, that it was nothing but ink on
paper. Since the 1997 mad cow feed ban in the USA, literally tons and tons of
banned mad cow feed has been put out into commerce, never to return, as late as
December of 2013, serious, serious breaches in the FDA mad cow feed ban have
been documented. The 2004 enhanced BSE surveillance program was so flawed, that
one of the top TSE prion Scientist for the CDC, Dr. Paul Brown stated ; Brown,
who is preparing a scientific paper based on the latest two mad cow cases to
estimate the maximum number of infected cows that occurred in the United States,
said he has "absolutely no confidence in USDA tests before one year ago" because
of the agency's reluctance to retest the Texas cow that initially tested
positive.
see ;
The BSE surveillance and testing have also been proven to be flawed, and
the GAO and OIG have both raised serious question as to just how flawed it has
been (see GAO and OIG reports). North America has more documented TSE prion
disease, in different documented species (excluding the Zoo BSE animals in the
EU), then any other place on the Globe. This does not include the very
likelihood that TSE prion disease in the domestic feline and canine have been
exposed to high doses of the TSE prion disease vid pet food. To date, it’s still
legal to include deer from cwd zone into pet food or deer food. Specified Risk
Material i.e. SRM bans still being breach, as recently as just last month.
nvCJD or what they now call vCJD, another case documented in Texas last
month, with very little information being released to the public on about this
case? with still the same line of thought from federal officials, ‘it can’t
happen here’, so another vCJD blamed on travel of a foreign animal disease from
another country, while ignoring all the BSE TSE Prion risk factors we have here
in the USA and Canada, and the time that this victim and others, do spend in the
USA, and exposed to these risk factors, apparently do not count in any way with
regard to risk factor. a flawed process of risk assessment.
sporadic CJD, along with new TSE prion disease in humans, of which the
young are dying, of which long duration of illness from onset of symptoms to
death have been documented, only to have a new name added to the pot of prion
disease i.e. sporadic GSS, sporadic FFI, and or VPSPR. I only ponder how a
familial type disease could be sporadic with no genetic link to any family
member? when the USA is the only documented Country in the world to have
documented two different cases of atypical H-type BSE, with one case being
called atypical H-G BSE with the G meaning Genetic, with new science now showing
that indeed atypical H-type BSE is very possible transmitted to cattle via oral
transmission (Prion2014). sporadic CJD and VPSPR have been rising in Canada,
USA, and the UK, with the same old excuse, better surveillance. You can only use
that excuse for so many years, for so many decades, until one must conclude that
CJD TSE prion cases are rising. a 48% incease in CJD in Canada is not just a
blip or a reason of better surveillance, it is a mathematical rise in numbers.
More and more we are seeing more humans exposed in various circumstance in the
Hospital, Medical, Surgical arenas to the TSE Prion disease, and at the same
time in North America, more and more humans are becoming exposed to the TSE
prion disease via consumption of the TSE prion via deer and elk, cattle, sheep
and goats, and for those that are exposed via or consumption, go on to further
expose many others via the iatrogenic modes of transmission of the TSE prion
disease i.e. friendly fire. I pondered this mode of transmission via the victims
of sporadic FFI, sporadic GSS, could this be a iatrogenic event from someone
sub-clinical with sFFI or sGSS ? what if?
Two decades have passed since Dr. Ironside first confirmed his first ten
nvCJD victims in 1995. Ten years later, 2005, we had Dr. Gambetti and his first
ten i.e. VPSPR in younger victims. now we know that indeed VPSPR is
transmissible. yet all these TSE prion disease and victims in the USA and Canada
are being pawned off as a spontaneous event, yet science has shown, the
spontaneous theory has never been proven in any natural case of TSE prion
disease, and scientist have warned, that they have now linked some sporadic CJD
cases to atypical BSE, to atypical Scrapie, and to CWD, yet we don’t here about
this in the public domain. We must make all human and animal TSE prion disease
reportable in every age group, in ever state and internationally, we must have a
serious re-evaluation and testing of the USA cattle herds, and we must ban
interstate movement of all cervids. Any voluntary effort to do any of this will
fail. Folks, we have let the industry run science far too long with regards to
the TSE prion disease. While the industry and their lobbyist continues to funnel
junk science to our decision policy makers, Rome burns. ...end
REFERENCES
Sunday, June 29, 2014
Transmissible Spongiform Encephalopathy TSE Prion Disease North America
2014
Tuesday, August 12, 2014
MAD COW USDA TSE PRION COVER UP or JUST IGNORANCE, for the record AUGUST
2014
Sunday, July 06, 2014
Dietary Risk Factors for Sporadic Creutzfeldt-Jakob Disease: A Confirmatory
Case-Control Study
Conclusions—The a priori hypotheses were supported.
*Consumption of various meat products may be one method of transmission of
the infectious agent for sCJD.
PLEASE NOTE, all url links linked as ;
have changed to ;
Sunday, January 19, 2014
*** National Prion Disease Pathology Surveillance Center Cases Examined1 as
of January 8, 2014
Thursday, February 21, 2013
*** National Prion Disease Pathology Surveillance Center Cases Examined
January 16, 2013
Monday, July 23, 2012
*** The National Prion Disease Pathology Surveillance Center July 2012
Friday, April 15, 2011
*** PRION TRANSMISSIBLE SPONGIFORM ENCEPHALOPATHY PROJECTS, RESEARCH
FUNDING, BSE VOLUNTARY TESTING UPDATE IN NORTH AMERICA 2011
Monday, August 9, 2010
*** National Prion Disease Pathology Surveillance Center Cases Examined
(July 31, 2010)
Sunday, May 16, 2010
*** The Final Report of the National Prion Research Program 2007 (updated
2010)
Monday, April 5, 2010
*** UPDATE - CJD TEXAS 38 YEAR OLD FEMALE WORKED SLAUGHTERING CATTLE
EXPOSED TO BRAIN AND SPINAL CORD MATTER
Friday, March 12, 2010
*** CJD 2010 and the CJD Foundation Family Conference
Saturday, January 2, 2010
*** Human Prion Diseases in the United States January 1, 2010
Monday, April 20, 2009
*** National Prion Disease Pathology Surveillance Center Cases Examined1
(December 31, 2008)
Sunday, April 12, 2009
*** r-calf and the USA mad cow problem, don't look, don't find, and then
blame Canada
Saturday, April 11, 2009
*** CJD FOUNDATION SIDES WITH R-CALFERS NO BSE OR HUMAN TSE THERE OF IN USA
'don't be fooled'
Sunday, April 20, 2008
*** Progress Report from the National Prion Disease Pathology Surveillance
Center April 3, 2008
Terry S. Singeltary Sr. P.O. Box 42 Bacliff, Texas USA 77518
flounder9@verizon.net
