Monday, November 3, 2014

USA CJD TSE PRION UNIT, TEXAS, SURVEILLANCE UPDATE NOVEMBER 2014

National Prion Disease Pathology Surveillance Center Cases Examined1 (October 7, 2014)

 

1 Listed based on the year of death or, if not available, on year of referral;

 

2 Cases with suspected prion disease for which brain tissue and/or blood (in familial cases) were submitted;

 

3 Disease acquired in the United Kingdom;

 

4 Disease acquired in the United Kingdom in one case and in Saudi Arabia in the other;

 

5 Disease possibly acquired in a Middle Eastern or Eastern European country;

 

6 Includes 11 cases in which the diagnosis is pending, and 19 inconclusive cases;

 

7 Includes 12 (11 from 2014) cases with type determination pending in which the diagnosis of vCJD has been excluded.

 

The sporadic cases include 2660 cases of sporadic Creutzfeldt-Jakob disease (sCJD),

 

50 cases of Variably Protease-Sensitive Prionopathy (VPSPr)

 

and 21 cases of sporadic Fatal Insomnia (sFI).

 

Year Total Referrals2 Prion Disease Sporadic Familial Iatrogenic vCJD

 

1996 & earlier 53 35 31 4 0 0

 

1997 114 68 59 9 0 0

 

1998 88 52 44 7 1 0

 

1999 123 74 65 8 1 0

 

2000 145 103 89 14 0 0

 

2001 212 120 110 10 0 0

 

2002 248 149 126 21 2 0

 

2003 265 167 137 30 0 0

 

2004 326 187 164 22 0 13

 

2005 343 194 157 36 1 0

 

2006 381 194 164 28 0 24

 

2007 377 213 184 29 0 0

 

2008 397 233 208 25 0 0

 

2009 421 255 213 41 1 0

 

2010 414 258 217 41 0 0

 

2011 410 256 215 41 0 0

 

2012 421 253 218 35 0 0

 

2013 439 280 221 57 1 0

 

2014 275 166 109 45 0 15

 

TOTAL 54526 32577 2731 503 7 4

 
http://www.cjdsurveillance.com/pdf/web_table.pdf


if you notice, if you add up the vpspr 50 cases and the sporadic FFI 21 cases, and then add to the total sporadic cjd cases of 2660, this is where the total of 2731 sporadic cases come from...seems they are lumping them all together as total sporadic cjd cases, and leaving the sporadic cjd text completly out of the picture now. smoooth. covering all bases I presume, and they moved the goal post in the middle of the game, again. niice...we all didn't fall off a shrimp boat yesterday$$$
 
 
 

 
Prion Disease Cases in Texas by Year, 2003-2012
Prion Disease Case Counts 2012
 
 
CJD_Graph_2012
 
CJD Age 2012
 
 
 
Last updated September 17, 2013
 
TEXAS CJD TSE PRION DISEASE SEE MAP ;
 
 
USA 4TH CASE VCJD (aka nvCJD) HUMAN MAD COW, THE SILENCE IS DEAFENING BSE, CWD, AND SCRAPIE TSE PRION DISEASE
 
Greetings DSHS, Dr. Fishcer, et al,
 
I know that most in the USA could care less about the CJD TSE prion disease aka mad cow type disease. but there are some of us here that will never forget.
 
you can cover up what ever you want. we all know. I have seen it happen too many times here in Texas with BSE TSE prion, either the typical or the atypical strains, or with the feed, or, with cwd, or scrapie as that goes, but we are still here, and we will never forget...
 
kind regards, terry
 
Creutzfeld-Jacob Disease (CJD) Emerging & Acute Infectious Disease Branch Michael Fischer
 
Marilyn Felkner
 
512-776-7676
 
512-776-7676
 
Chronic Wasting Disease Zoonosis Control Branch Eric Fonken
 
512-776-2155
 
Lab tests have confirmed a diagnosis of variant Creutzfeldt-Jakob Disease (CJD) in a patient who recently died in Texas. Variant CJD is a rare, fatal brain disorder, first described in 1996 in the United Kingdom and associated with beef consumption overseas.
 
This is the fourth case ever reported in the United States. In each of the three previous cases, infection likely occurred outside the United States, including the United Kingdom and Saudi Arabia. The history of this fourth patient includes extensive travel to Europe and the Middle East, and infection likely occurred outside the United States. The CDC and DSHS continue to investigate the case.
 
There are no Texas public health concerns or threats associated with this case.
 
 
 
 
Last updated June 02, 2014
 
 
CONFIRMED HUMAN BSE AKA MAD COW DISEASE vCJD TEXAS USA
 
CONFIRMED HUMAN BSE AKA MAD COW DISEASE vCJD TEXAS USA
 
Monday, June 02, 2014 Confirmed Variant CJD Case in Texas
 
 
SO, 4 months after the fact and still no word on this case. no information what so ever. the silence is deafening $$$
 
Monday, November 3, 2014
 
The prion protein protease sensitivity, stability and seeding activity in variably protease sensitive prionopathy brain tissue suggests molecular overlaps with sporadic Creutzfeldt-Jakob disease
 
 
 
 
Saturday, August 14, 2010
 
BSE Case Associated with Prion Protein Gene Mutation (g-h-BSEalabama) and VPSPr PRIONPATHY
 
 
Monday, June 23, 2014
 
PRION 2014 TYPICAL AND ATYPICAL BSE AND CJD REPORT UPDATES
 
 
 Transmissible Spongiform Encephalopathy TSE Prion Disease North America 2014
 
Transmissible Spongiform Encephalopathy TSE Prion Disease have now been discovered in a wide verity of species across North America. typical C-BSE, atypical L-type BASE BSE, atypical H-type BSE, atypical H-G BSE, of the bovine, typical and atypical Scrapie strains, in sheep and goats, with atypical Nor-98 Scrapie spreading coast to coast in about 5 years. Chronic Wasting Disease CWD in cervid is slowly spreading without any stopping it in Canada and the USA and now has mutated into many different strains. Transmissible Mink Encephalopathy TME outbreaks. These Transmissible Spongiform Encephalopathy TSE Prion Disease have been silently mutating and spreading in different species in North America for decades.
 
The USDA, FDA, et al have assured us of a robust Triple BSE TSE prion Firewall, of which we now know without a doubt, that it was nothing but ink on paper. Since the 1997 mad cow feed ban in the USA, literally tons and tons of banned mad cow feed has been put out into commerce, never to return, as late as December of 2013, serious, serious breaches in the FDA mad cow feed ban have been documented. The 2004 enhanced BSE surveillance program was so flawed, that one of the top TSE prion Scientist for the CDC, Dr. Paul Brown stated ; Brown, who is preparing a scientific paper based on the latest two mad cow cases to estimate the maximum number of infected cows that occurred in the United States, said he has "absolutely no confidence in USDA tests before one year ago" because of the agency's reluctance to retest the Texas cow that initially tested positive.
 
see ;
 
 
The BSE surveillance and testing have also been proven to be flawed, and the GAO and OIG have both raised serious question as to just how flawed it has been (see GAO and OIG reports). North America has more documented TSE prion disease, in different documented species (excluding the Zoo BSE animals in the EU), then any other place on the Globe. This does not include the very likelihood that TSE prion disease in the domestic feline and canine have been exposed to high doses of the TSE prion disease vid pet food. To date, it’s still legal to include deer from cwd zone into pet food or deer food. Specified Risk Material i.e. SRM bans still being breach, as recently as just last month.
 
nvCJD or what they now call vCJD, another case documented in Texas last month, with very little information being released to the public on about this case? with still the same line of thought from federal officials, ‘it can’t happen here’, so another vCJD blamed on travel of a foreign animal disease from another country, while ignoring all the BSE TSE Prion risk factors we have here in the USA and Canada, and the time that this victim and others, do spend in the USA, and exposed to these risk factors, apparently do not count in any way with regard to risk factor. a flawed process of risk assessment.
 
sporadic CJD, along with new TSE prion disease in humans, of which the young are dying, of which long duration of illness from onset of symptoms to death have been documented, only to have a new name added to the pot of prion disease i.e. sporadic GSS, sporadic FFI, and or VPSPR. I only ponder how a familial type disease could be sporadic with no genetic link to any family member? when the USA is the only documented Country in the world to have documented two different cases of atypical H-type BSE, with one case being called atypical H-G BSE with the G meaning Genetic, with new science now showing that indeed atypical H-type BSE is very possible transmitted to cattle via oral transmission (Prion2014). sporadic CJD and VPSPR have been rising in Canada, USA, and the UK, with the same old excuse, better surveillance. You can only use that excuse for so many years, for so many decades, until one must conclude that CJD TSE prion cases are rising. a 48% incease in CJD in Canada is not just a blip or a reason of better surveillance, it is a mathematical rise in numbers. More and more we are seeing more humans exposed in various circumstance in the Hospital, Medical, Surgical arenas to the TSE Prion disease, and at the same time in North America, more and more humans are becoming exposed to the TSE prion disease via consumption of the TSE prion via deer and elk, cattle, sheep and goats, and for those that are exposed via or consumption, go on to further expose many others via the iatrogenic modes of transmission of the TSE prion disease i.e. friendly fire. I pondered this mode of transmission via the victims of sporadic FFI, sporadic GSS, could this be a iatrogenic event from someone sub-clinical with sFFI or sGSS ? what if?
 
Two decades have passed since Dr. Ironside first confirmed his first ten nvCJD victims in 1995. Ten years later, 2005, we had Dr. Gambetti and his first ten i.e. VPSPR in younger victims. now we know that indeed VPSPR is transmissible. yet all these TSE prion disease and victims in the USA and Canada are being pawned off as a spontaneous event, yet science has shown, the spontaneous theory has never been proven in any natural case of TSE prion disease, and scientist have warned, that they have now linked some sporadic CJD cases to atypical BSE, to atypical Scrapie, and to CWD, yet we don’t here about this in the public domain. We must make all human and animal TSE prion disease reportable in every age group, in ever state and internationally, we must have a serious re-evaluation and testing of the USA cattle herds, and we must ban interstate movement of all cervids. Any voluntary effort to do any of this will fail. Folks, we have let the industry run science far too long with regards to the TSE prion disease. While the industry and their lobbyist continues to funnel junk science to our decision policy makers, Rome burns. ...end
 
REFERENCES
 
Sunday, June 29, 2014
 
Transmissible Spongiform Encephalopathy TSE Prion Disease North America 2014
 
 
Tuesday, August 12, 2014
 
MAD COW USDA TSE PRION COVER UP or JUST IGNORANCE, for the record AUGUST 2014
 
 
Sunday, July 06, 2014
 
Dietary Risk Factors for Sporadic Creutzfeldt-Jakob Disease: A Confirmatory Case-Control Study
 
Conclusions—The a priori hypotheses were supported.
 
*Consumption of various meat products may be one method of transmission of the infectious agent for sCJD.
 
 
 PLEASE NOTE, all url links linked as ;
 
 
 have changed to ;
 
 
 Sunday, January 19, 2014
 
*** National Prion Disease Pathology Surveillance Center Cases Examined1 as of January 8, 2014
 
 
 Thursday, February 21, 2013
 
 *** National Prion Disease Pathology Surveillance Center Cases Examined January 16, 2013
 
 
 Monday, July 23, 2012
 
*** The National Prion Disease Pathology Surveillance Center July 2012
 
 
 Friday, April 15, 2011
 
*** PRION TRANSMISSIBLE SPONGIFORM ENCEPHALOPATHY PROJECTS, RESEARCH FUNDING, BSE VOLUNTARY TESTING UPDATE IN NORTH AMERICA 2011
 
 
Monday, August 9, 2010
 
*** National Prion Disease Pathology Surveillance Center Cases Examined (July 31, 2010)
 
 
Sunday, May 16, 2010
 
*** The Final Report of the National Prion Research Program 2007 (updated 2010)
 
 
Monday, April 5, 2010
 
*** UPDATE - CJD TEXAS 38 YEAR OLD FEMALE WORKED SLAUGHTERING CATTLE EXPOSED TO BRAIN AND SPINAL CORD MATTER
 
 
Friday, March 12, 2010
 
*** CJD 2010 and the CJD Foundation Family Conference
 
 
 Saturday, January 2, 2010
 
 *** Human Prion Diseases in the United States January 1, 2010
 
 
Monday, April 20, 2009
 
*** National Prion Disease Pathology Surveillance Center Cases Examined1 (December 31, 2008)
 
 
Sunday, April 12, 2009
 
*** r-calf and the USA mad cow problem, don't look, don't find, and then blame Canada
 
 
 Saturday, April 11, 2009
 
*** CJD FOUNDATION SIDES WITH R-CALFERS NO BSE OR HUMAN TSE THERE OF IN USA 'don't be fooled'
 
 
 Sunday, April 20, 2008
 
*** Progress Report from the National Prion Disease Pathology Surveillance Center April 3, 2008
 
 
 
Terry S. Singeltary Sr. P.O. Box 42 Bacliff, Texas USA 77518 flounder9@verizon.net
 
 
 
 
 
 
 
 
 
 
 




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